ABSTRACT
Testicular tumors are relatively uncommon in children. The tumors of germ cell origin are still frequently encountered. The pure embryonal rhabdomyosarcomas of testis, not associated with sarcomatous component of the germ cell tumor, is a very rare entity. It is a highly aggressive tumor of childhood and young adolescents. In testes, it arises commonly from paratesticular tissue; primary intratesticular being extremely rare. To the best of authors knowledge, only fifteen cases of primary pure intratesticular tumor have been reported in the literature so far. We report a case of eight-year-old child who presented with a progressive painless right testicular enlargement over two months. Ultrasonography showed a heterogenous intratesticular mass. High orchidectomy was performed. Histopathological examination of the specimen assisted with immunohistochemistry revealed embryonal rhabdomyosarcoma.
ABSTRACT
Objective@#To report a rare case of epididymal liposarcoma with multiple metastases to the retroperitoneal space and peritoneal cavity for the purpose of improving the diagnosis and treatment of the disease.@*METHODS@#We retrospectively analyzed the clinical data about a case of epididymal liposarcoma with multiple metastases to the retroperitoneal space and peritoneal cavity, reviewed relevant literature at home and abroad, and investigated the presentation, diagnosis and treatment of the disease.@*RESULTS@#A 47-year-old male patient with epididymal liposarcoma underwent radical left orchiectomy with high ligation of the spermmatic cord. Ten years later, recurrence and metastasis were observed in the retroperitoneal space with a mass of 15.6 × 9.4 × 25.5 cm occupying an area from the upper pole of the left kidney to the pelvic cavity and enclosing the left kidney and upper ureter, for which the patient received radical resection of the retroperitoneal tumor. However, multiple retroperitoneal and intraperitoneal metastases occurred again 4 years later, which was treated by another surgical resection. The patient died of lung failure a year later.@*CONCLUSIONS@#Epididymal liposarcoma is a rare entity, which can be diagnosed by careful clinical and radiological examinations and confirmed by pathology. For its treatment, radical inguinal orchiectomy should be performed as early as possible, but the roles of adjuvant radiotherapy and chemotherapy remain controversial. Given the high rate of recurrence and metastasis, long-term follow-up is necessitated for the patient postoperatively.
Subject(s)
Humans , Male , Middle Aged , Epididymis , Pathology , Genital Neoplasms, Male , Pathology , Kidney , Liposarcoma , Pathology , Neoplasm Recurrence, Local , Orchiectomy , Peritoneal Cavity , Peritoneal Neoplasms , Retroperitoneal Neoplasms , Retroperitoneal SpaceABSTRACT
A liposarcoma of paratesticular origin is extremely rare, and preoperative diagnosis is difficult. Most are a low-grade malignancy. We report a case of a mixed liposarcoma of the paratesticular tissues in a 74-year-old man. Treatment consisted of a radical orchiectomy without retroperitoneal lymph node dissection. The patient has survived 18 months with no evidence of a recurrence.
Subject(s)
Aged , Humans , Diagnosis , Liposarcoma , Lymph Node Excision , Orchiectomy , RecurrenceABSTRACT
Primary tumors of the spermatic cord are rare and basically of connective tissue origin. They are hardly ever considered in the differential diagnosis of intrascrotal swellings. Treatment consisted of radical orchiectomy without retroperitoneal lymph node dissection, and adjuvant radiation and chemotherapy. We report a case of liposarcoma of the spermatic cord in 54-year-old male. He has survived l5 months without evidence of recurrence.
Subject(s)
Humans , Male , Middle Aged , Connective Tissue , Diagnosis, Differential , Drug Therapy , Liposarcoma , Lymph Node Excision , Orchiectomy , Recurrence , Spermatic CordABSTRACT
Liposarcoma of paratesticular origin is extremely rare and preoperative diagnosis is unusual. Myxoid type or liposarcoma is in general less malignant than testicular tumor and orchiectomy with high ligation and wide excision of tumor mass are probably the treatment of choice. We are present a case of myxoid liposarcoma and reviewed literatures.
Subject(s)
Diagnosis , Ligation , Liposarcoma , Liposarcoma, Myxoid , OrchiectomyABSTRACT
Liposarcoma of paratesticular origin is extremely rare and preoperative diagnosis is unusual. Myxoid type or liposarcoma is in general less malignant than testicular tumor and orchiectomy with high ligation and wide excision of tumor mass are probably the treatment of choice. We are present a case of myxoid liposarcoma and reviewed literatures.
Subject(s)
Diagnosis , Ligation , Liposarcoma , Liposarcoma, Myxoid , OrchiectomyABSTRACT
A clinical observation was made on 19 cases of paratesticular tumors in 19 patients which were neither resolved nor improved with primary medical and conservative treatment in the Department of Urology. Capital Armed Forces General Hospital during the period from March, 1977 to July, 1981. The following results were obtained. 1. The age was ranged from 20 to 45 years old and the most favorable age was in 3rd decade. 2. The main symptoms and signs were palpable mass in 73.1%. 3. Duration of symptoms from onset was over 1 year in 57.9% and under 1 year in 42.1%. The mean duration was 17 months. 4. Organ distribution was 5 cases in epididymis, 5 in spermatic cord and 9 in scrotal tunics. 5. 11 cases arose on the left side, 4 on the right and 4 on the midline. 6. There were benign tumors in 17 (89.5%) and malignant tumors only in 2 (10.5%) of all 19 cases. These malignant lesions were developed in the spermatic cord. 7. The lesions were managed by local resection in 16 cases, orchiectomy in 2 and epididymectomy in 1.